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KÜÇÜK LENFOSİTİK LENFOMA (SLL)


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Medicine and Hematology Glossary

KÜÇÜK LENFOSİTİK LENFOMA (SLL)

(Medicine and Hematology Glossary) :
Tüm HDL'nın %5'den azıdır. İleri yaş hastalığıdır. Mitoz hızı düşük, matür görünüşlü, küçük lenfositlerden oluşur. Hücreler B lenfosit işaretleri olan CD19+, CD20+'dir. Diğer özellikleri CD5+, CD23+, CD43+ olmalıdır. CD10 - 'dir. Lenf bezinde medüller kordlardaki lenfositlerden oluşurlar. Bu hücreler resirkülasyon yapan CD5+, CD23+ periferik B lenfositler olarak kabul edilmektedir. Yaklaşık %90 olguda kemik iliği tutulumu vardır. SLL'de orbita, akciğer, cilt ve midede ekstranodal tutulum olabilir. Bazı olgularda serumda monoklonal protein saptanır. %40 olguda tümör hücreleri periferik dolaşıma geçer ve kronik lenfostik lösemiyi (KLL) andırır. B tipi KLL ile kinik semptomlar ve muayene bulguları bakımından da benzerlik gösterir. Lenf bezi kesitlerinde her iki hastalıkta da iyi diferansiye lenfosit infitrasyonu vardır ve morfolojik olarak birbirinden ayırdedilemezler. SLL hücrelerinde LFA-1 pozitif KLL'de negatif oluşu da tanıya yardımcıdır. SLL büyük hücreli lenfomaya transforme olabilir (Richter sendromu).
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